NUT Carcinoma

NUT carcinoma, also known as midline tract cancer or NUT midline carcinoma, is a rare type of carcinoma that is caused by a genetic mutation. More specifically, it is caused by the fusion of the NUTM1 (nuclear protein in testis) gene with another gene, most commonly the BRD4 (bromodomain containing 4) gene. This fusion may result in the production of an oncoprotein (proteins associated with the growth of cancer cells), causing a tumour to grow. The NUTM1 gene is found on chromosome 15 and is responsible for the production of specific proteins.

NUT carcinoma often develops from the squamous cells lining organs. It is most commonly found in the head, neck, and lungs. However, it can also develop in the organs of the mediastinum or the stomach.

Despite the name of the gene, this type of cancer develops equally in the sexes. It is commonly found in children, but can be diagnosed at any age.

Treatment

Due to the rarity of NUT carcinoma, there is no standard staging and grading system for this disease. Your doctor will check for signs of metastasis, and how the cancer cells look under the microscope to help guide treatment options.

Your doctor may also recommend genetic testing, which analyses your tumour DNA and can help determine which treatment has the greatest chance of success. They will then discuss the most appropriate treatment option for you.

Treatment is dependent on several factors, including location, stage of disease and overall health.

Treatment options for NUT carcinoma may include:

  • Surgery – surgical options will vary based on tumour location.
  • Radiation therapy.
  • Chemotherapy.
  • Clinical trials.
  • Palliative care.

Risk factors

Because of how rare NUT carcinoma is, there has been limited research done into the risk factors of this disease.

Symptoms

The symptoms of NUT Carcinoma may vary based on location.

General symptoms may include:

  • Unexplainable weight loss.
  • Fatigue.
  • Pain in the affected area.
  • Dyspnea.
  • Persistent cough.
  • Coughing up blood.
  • Pleural effusion.

Not everyone with the symptoms above will have cancer but see your general practitioner (GP) if you are concerned.

Diagnosis/diagnosing

If your doctor suspects you have NUT carcinoma, they may order the following tests to confirm the diagnosis and refer you to a specialist for treatment:

  • Physical examination.
  • Imaging tests, potentially including:
    • MRI (magnetic resonance imaging).
    • CT (computed tomography) scan.
    • PET (positron emission tomography) scan.
  • Blood tests.
  • Pulmonary function test.
  • Sputum cytology.
  • Biopsy.

References

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