call 1800 257 600 email [email protected]

Leptomeningeal Metastases

Leptomeningeal metastases, also known as leptomeningeal disease, carcinomatous meningitis or meningeal carcinomatosis, is a rare complication of advanced cancers where malignant or cancerous cells spread to the two inner most layers of tissue that cover the brain and the spinal cord (known as leptomeninges) and cerebrospinal fluid (CSF). It most commonly occurs as a result of breast cancer, lung cancer or cutaneous melanoma, however, can also develop as a result of other malignancies such as gastrointestinal or haematological cancers.

There are three primary membranes that make up the meninges: the dura mater, the arachnoid and the pia mater. The dura mater is the thick, membranous, outermost layer of the meninges located directly under the skull. Its main functions are to provide structural support, anchor the central nervous system (CNS) and assist in regulating CSF circulation. The arachnoid is the middle layer of the meninges. Its main function is to cushion the brain and spinal cord from trauma, and facilitate the circulation of CSF. The pia mater is the innermost layer of the meninges, and its main functions are to act as a barrier to protect the CNS from contaminants, and allowing the passage of small blood vessels that nourish the brain.

It is currently unknown whether leptomeningeal metastases is likely to affect one sex more than another, and it is difficult to determine an average age of diagnosis as it is a rare, late-stage complication of different types of cancer. However, it is thought that anyone can develop this disease.

Treatment

When cancers are detected, they are staged and graded based on size, metastasis, and how the cancer cells look under the microscope. Staging and grading helps your doctors determine the best treatment for you. However, as leptomeningeal metastases is often a complication of late-stage or metastatic cancer, it is automatically classified as stage IV disease.

Treatment options for leptomeningeal metastases are often palliative, and may include:

  • Shunt insertion
  • Radiation therapy
  • Intrathecal chemotherapy
  • Immunotherapy (limited)
  • Clinical trials
  • Palliative care

Risk factors

Because of how rare leptomeningeal metastases is, there has been limited research done into the risk factors of this disease.

Symptoms

Symptoms of leptomeningeal metastases may include:

  • Headaches.
  • Nausea and/or vomiting.
  • Light-headedness or dizziness.
  • Encephalopathy, which may include:
    • Confusion.
    • Forgetfulness.
    • Disorientation.
    • Behavioural changes.
    • Lethargy.
  • Diplopia
  • Facial pain, weakness, tingling and/or numbness
  • Hearing changes and/or loss
  • Seizures
  • Facial drooping
  • pain in your lower back, legs or neck
  • Difficulties speaking
  • Dysphagia (difficulties swallowing)
  • Poor balance
  • Difficulties walking
  • Incontinence

Not everyone with the symptoms above will have cancer, but see your general practitioner (GP) if you are concerned.

Diagnosis

If your doctor suspects you have leptomeningeal metastases, they may order the following tests to confirm the diagnosis and refer you to a specialist for treatment:

  • Physical examination.
  • Neurological examination
  • Imaging studies, most commonly an magnetic resonance imaging (MRI) scan of the brain and/or spine
  • Lumbar puncture

References

Keep up with Rare Cancers Australia

Inside Rare is a monthly newsletter that shares the latest news, events and stories connecting the rare community.